Abstract

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• PURPOSE:

  A case of the rare, benign, Wilms' tumor (WT) variant, metanephric adenofibroma (MAF), is presented.

  MATERIALS AND METHODS:

  The patient is a 21-year-old female with an incidentally discovered enhancing renal mass. The diagnosis, workup and treatment are outlined.

  RESULTS:

  The 19 cm renal mass was ultimately resected via robot-assisted partial nephrectomy. Pathologic diagnosis at our institution was confirmed as a MAF by the National Wilms' Tumor Study Group (NWTSG).

  CONCLUSION:

  Difficult to differentiate from WT, it is imperative that MAF be recognized and appropriately diagnosed because unlike adult WT, the natural history of MAF is indolent and adjuvant chemo/radiation therapy is rarely necessary. This case reinforces the importance of review of potential WT variants by the NWTSG.