Abstract

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• Wilms tumor (WT) is the most common primary malignant renal tumor in children and usually presents as an abdominal mass. Rhabdomyomatous nephroblastoma is a rare histologic variant of WT. Herein we report an unusual case of WT with rhabdomyomatous differentiation presenting with hematuria and the passage of tissue via the urethra in a 2-year-old male.